Acquired hemophilia A: case report

Česká verze

Authors: Štefan Sotak ¹; Miriam Mitníková ²
Authors place of work: I. interná klinika LF UPJŠ a UN L. Pasteura Košice, Slovenská republika ¹; Oddelenie labortórnej medicíny LF UPJŠ a UN L. Pasteura Košice, Slovenská republika ²
Published in the journal: Vnitř Lék 2018; 64(4): 427-431
Category: Kazuistiky

Summary

Case report of a 74-year-old male with acquired hemophilia A, whose etiology was not found, confirmed by hemocoagulation examinations, with clinical manifestation of protracted macroscopic hematuria, spontaneous skin and intramuscular bleedings. Treatment comprised conservative therapy administration of hemostyptics, red blood cells transfusions application of recombinant human factor VII (rFVII) and immunosuppression. Finally, patient died due to nosocomial infection caused by multidrug-resistant pulmonary pathogen.

Key words:
acquired hemophilia A – bleeding

Zdroje

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