Weber-Christian disease: a case report

Česká verze

Authors: Kristína Brázdilová ¹; Daniel Čierny ¹; Katarína Hrubišková ¹; Lukáš Plank ²; Zdenko Killinger ¹; Juraj Payer ¹
Authors place of work: V. interná klinika LF UK a UNB, Nemocnica Ružinov, Bratislava, Slovenská republika ¹; Ústav patologickej anatómie JLF UK a UNM, Martin, Slovenská republika ²
Published in the journal: Vnitř Lék 2018; 64(10): 961-965
Category: Kazuistika

Summary

Weber-Christian disease is a rare disease from the group of chronic fibrosing conditions characterized by inflammation of the adipose tissue –⁠ panniculitis and fibrosing with frequent systemic manifestations. Etiopathogenesis of the disease is not fully known, participation of autoimmune mechanisms is anticipated. Here, we report a case of a patient with this rare disease, diagnosed after a long and demanding diagnostic process, including repeated laparotomies. However, after immunosuppressive therapy, clinical and laboratory symptomatology improved rapidly as well as the patient’s quality of life.

Key words:

panniculitis –⁠ sclerosing mesenteritis –⁠ Weber-Christian disease

Zdroje

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