Life threatening manifestations of connective tissue diseases and vasculitides

Authors: J. Vymětal;  P. Horák;  M. Skácelová
Authors‘ workplace: III. interní klinika, nefrologická, revmatologická, endokrinologická, FN a LF UP Olomouc
Published in: Čes. Revmatol., 23, 2015, No. 3, p. 100-113.
Category: Review Article


Rheumatic diseases may be presented at onset or in the course of diseases by acute serious illness, even life threatening and requiring admission to intensive care unit. The spectrum of symptoms and organs involvement is very wide, so as it corresponds to systemic character of diseases, which are the primary domain of rheumatology, but it also places high demands on knowledge of possible differential diagnosis of doctors working at intensive wards. This article gives an overview of most acute situation, which physicians can meet in patients with systemic diseases, including lupus erythematosus, antiphospolipid syndrome, systemic scleroderma, dermatomyositis/polymyositis and individual types of vasculitides group.

Key words:
Life-threatening events, SLE, antiphospholipid syndrome, scleroderma, idiopatic myositis, vasculitis


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