Recommendations of the Czech Society for Rheumatology for the treatment of systemic sclerosis.

Authors: R. Bečvář 1;  T. Soukup 2;  M. Tomčík 1;  P. Jansa 3
Authors‘ workplace: Revmatologický ústav, Revmatologická klinika 1. LF UK 1;  II. interní gastroenterologická klinika, Fakultní nemocnice LF UK, Hradec Králové 2;  II. interní klinika kardiologie a angiologie a Všeobecná fakultní nemocnice, 1. LF UK, Praha 3
Published in: Čes. Revmatol., 25, 2017, No. 2, p. 68-84.
Category: Recommendation


Systemic sclerosis (SSc) involves skin, blood vessels and different visceral organs and leads to sclerotisation and fibrosis which results in development of irreversible functional and structural changes. EUSTAR/EULAR group which addresses basic and clinical research of SSc has formulated recommendations for the treatment of SSc based on data that can be used in clinical practice. Management of SSc should be complex including early diagnostics of visceral organ involvement, selection of patients with high risk of progression and also non-pharmacological methods. In 2009 14 recommendations for therapy of different SSc organ manifestations were published and later in 2016 these recommendations were updated to 16 items. In 2016 more comprehensive recommendations of British Society for Rheumatology together with British Health Professionals In Rheumatology were published, which have in total 39 items. The main purpose of this article is to offer to clinical rheumatologists practical recommendations for treatment of SSc patients in current conditions of Czech Republic.

Systemic sclerosis, organ manifestations, recommendation, treatment, clinical trial.


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