Malignant Peripheral Nerve Sheath Tumour of Cervical Plexus –  a Case Report


Authors: Z. Kadaňka Jr 1;  J. Hanák 2;  B. Gál 2
Authors‘ workplace: Neurologická klinika LF MU a FN Brno 1;  ORL klinika LF MU a FN u sv. Anny v Brně 2
Published in: Cesk Slov Neurol N 2013; 76/109(6): 751-755
Category: Case Report

Overview

Malignant peripheral nerve sheath tumours are rare neoplasms, especially in the head and neck. They are often asymptomatic. We present a case of 29-years old patient with neurofibromatosis type 1 with malignant tumour of the cervical plexus. A small resistance in the upper mediastinum was diagnosed (ganglioneurinoma) in 2005 and treated surgically (total exstirpation). A small infiltration in the right supraclavicular area occurred five years later and was also managed surgically (debulking) – histologically MPNST. There was a relapse of this tumour in the same area in 2011; this was treated by en bloc resection, followed by chemotheraphy. At present, the patient is in a good clinical status, with no neurological deficit.

Key words:
malignant peripheral nerve sheath tumour – cervical plexus – malignant schwannoma – neurofibromatosis type 1

The authors declare they have no potential conflicts of interest concerning drugs, products, or services used in the study.

The Editorial Board declares that the manu­script met the ICMJE “uniform requirements” for biomedical papers.


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Labels
Paediatric neurology Neurosurgery Neurology

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Czech and Slovak Neurology and Neurosurgery

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