NEPHROBLASTOMA – CURRENT EVALUATION AND TREATMENT


Authors: Marcela Pýchová 1;  Karel Švojgr 2;  Josef Mališ 2;  Michal Rygl 1;  Karel Pýcha 1;  Martin Kynčl 3;  Roman Kodet 4;  Jan Starý 2;  Jiří Šnajdauf 1
Authors‘ workplace: Klinika dětské chirurgie 2. LF UK a FN Motol, Praha 1;  Klinika dětské hematoonkologie 2. LF UK a FN Motol, Praha 2;  Klinika zobrazovacích metod 2. LF UK a FN Motol, Praha 3;  Ústav patologie a molekulární medicíny 2. LF UK a FN Motol, Praha 4
Published in: Ces Urol 2016; 20(2): 113-122
Category: Review article

Overview

Nephroblastoma (Wilms tumor – WT) is the most common solid renal tumor in children. The patients are treated according to SIOP 2001 protocol. This protocol recommends pre-operative chemotherapy, nephrectomy and postoperative treatment. Blastemal and anaplastic histological subtypes are poor prognostic factors. It is a well treatable disease, with up to 90 % of patients cured.

Key words:
Nephroblastoma, therapy, Wilms´ tumor.


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Labels
Paediatric urologist Nephrology Urology

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