Cutis Marmorata Teleangiectatica Congenita


Authors: M. Komorousová;  K. Pizinger
Authors‘ workplace: Dermatovenerologická klinika FN a LF UK Plzeň přednosta prof. MUDr. Karel Pizinger, CSc.
Published in: Čes-slov Derm, 85, 2010, No. 6, p. 337-339
Category: Case Reports

Overview

Cutis marmorata teleangiectatica congenita (CMTC) is a rare, usually benign, vascular malformation of unknown etiology. It is present at birth or shortly thereafter. Improvement with age is common. Persistent form has been described rarely. Females are affected more commonly. The lesions are usually localized on the trunk and limbs. Ulceration and impetiginization are the most common complications. The incidence of associated abnormalities is high. The most frequent are psychomotor retardation, epilepsy, hypoplasia and hypertrophy of the affected limbs and eye anomalies. There is no causal treatment of the disease.

Our patient was a 3-months-old boy with lesions on the trunk and limbs present at birth. No changes of the clinical picture were observed in the postpartum period.

Key words:
cutis marmorata teleangiectatica congenita – vascular malformation


Sources

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Labels
Dermatology & STDs Paediatric dermatology & STDs
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