Zoon vulvitis –⁠ a rare form of chronic inflammation of the vulva

Czech version

Authors: A. Lavrov; P. Gráf; V. Unzeitig
Authors‘ workplace: Gynekologicko-porodnická klinika FN, Ostrava, přednosta doc. MUDr. O. Šimetka, Ph. D., MBA
Published in: Ceska Gynekol 2018; 83(4): 286-290
Category: Case Report

Overview

Objective: Description of finding out rare disease Zoon vullvitis.

Desing: Case report and differential diagnosis.

Setting: Department of Obstetric and Gynecology, University Hospital Ostrava.

Case report: Zoon vulvitis or plasma cell vulvitis (PCV) belongs to extremely rare and often misdiagnosed inflammatory disease of the vulva. Lesions may look like shiny, sharply bordered , erythematosus patches or macular lesions. Less than 50 cases have been reported. This article is devoted to clinical findings, differential diagnosis and treatment of PCV. We present one clinical case with typical clinical and histopathological manifestations. Risk of dysplasia exists and long-term follow-up is desirable.

Keywords: Zoon vullvitis, vulvar disease, differentional diagnosis, pruritus

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