Idiopathic pulmonary fibrosis – changes in dia­gnostics and treatment


Authors: Vašáková M.
Authors‘ workplace: Pneumologická klinika 1. LF UK a Thomayerovy nemocnice, Praha
Published in: Kardiol Rev Int Med 2019, 21(3): 135-141

Overview

Idiopathic pulmonary fibrosis (IPF) belongs to the most difficult-to-treat and most serious of lung diseases, with prognosis similar to lung cancer. Epidemiologic data are highly probably underestimated in many countries since IPF used to be frequently misdia­gnosed for other dia­gnoses or not dia­gnosed at all. In the last century, when described for the first time, IPF was an extremely rare dia­gnosis. Nowadays, the incidence of IPF is undoubtedly rising, which is also sup­ported by improved dia­gnostic opportunities. Previously, IPF was considered an untreatable disease; however, this has changed in the last eight years as antifibrotic therapy has emerged. Due to this fact, IPF patients have a better chance of survival, although the disease is still uncurable.

Keywords:

idiopathic pulmonary fibrosis – dia­gnosis


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Paediatric cardiology Internal medicine Cardiac surgery Cardiology
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