AL amyloidosis in pictures

Czech version

Authors: P. Látalová ¹; T. Pika ²; P. Flodr ¹
Authors‘ workplace: Ústav klinické a molekulární patologie LF UP v Olomouci ¹; Hemato-onkologická klinika FN Olomouc a LF UP v Olomouci ²
Published in: Transfuze Hematol. dnes,20, 2014, No. 3, p. 76-80.
Category: Comprehensive Reports, Original Papers, Case Reports

Overview

Patients with systemic AL amyloidosis are often diagnosed in advanced stages of the disease, although possibilities for detecting this disease and stratifying patients are still expanding and are not restricted only to specialized medical centres. This case report aims to draw attention to the topic from an unusual angle, namely that of the pathologist, supported by photo documentation. It details the case of a patient with greatly advanced disease, which was diagnosed only shortly before death in the stage of highly significant end-organ changes, three months following the first examination by a physician.

Key words:
AL amyloidosis, free light immunoglobulin chains, renal involvement, cardiac involvement

Sources

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