Eisenmenger syndrome and complications in children – case report

Czech version

Authors: T. Doušová ¹; J. David ¹; K. Špičáková ¹; K. Koubský ²; V. Koukolská ³; P. Jansa ⁴
Authors‘ workplace: Pediatrická klinika 2. lékařské fakulty Univerzity Karlovy a FN Motol, Praha ¹; Dětské kardiocentrum 2. lékařské fakulty Univerzity Karlovy a FN Motol, Praha ²; Klinika zobrazovacích metod 2. lékařské fakulty Univerzity Karlovy a FN Motol, Praha ³; Centrum pro plicní hypertenzi, 1. lékařská fakulta Univerzity Karlovy, Všeobecná fakultní nemocnice, Praha ⁴
Published in: Čes-slov Pediat 2020; 75 (3): 178-182.
Category: Case Report

Overview

3–10% patients with congenital heart disease (CHD) develop pulmonary arterial hypertension (PAH). The natural course of untreated CHD with significant left-to-right shunt is gradual increase in pulmonary vascular resistance, eventually resulting in reversal of the shunt (Eisenmenger syndrome, ES). PAH-CHD is associated with significant morbidity and mortality. Due to early diagnosis and surgical possibilities of CHD repair, there has been a significant decrease in number of patients with ES.

Authors present a case report of a fifteen-year-old boy with ES and a life-threatening complication – multiplex septic intracranial embolisation.

Keywords:

congenital heart disease – pulmonary arterial hypertension – Eisenmenger syndrome – cerebral abscess

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