A fatal complication of tracheostomy in a 13-year-old patient with Duchenne Muscular Dystrophy –⁠ case report

Czech version

Authors: Stříteská Jana ¹; Pařízková Renata ¹; Dostál Pavel ¹; Hoffmann Petr ²; Černý Vladimír ¹
Authors‘ workplace: Klinika anesteziologie, resuscitace a intenzivní medicíny, UK v Praze, LF v Hradci Králové, Fakultní nemocnice Hradec Králové ¹; Radiologická klinika, Fakultní nemocnice Hradec Králové ²
Published in: Anest. intenziv. Med., 20, 2009, č. 2, s. 107-112
Category: Intesive Care Medicine - Case Report

Overview

The authors describe a case of a 13-year-old boy suffering from Duchenne muscular dystrophy. Permanent mechanical ventilation was necessary due to the patient’s progressive chronic respiratory insufficiency. A surgical tracheostomy was complicated by the development of tracheal stenosis managed with special types of tracheostomy tubes. A tracheo-arterial fistula developed as a result of progression of skeletal chest deformities and the tracheal stenosis. The patient died of massive arterial haemorrhage from the fistula formed between the trachea and the brachiocephalic trunk.

Keywords:
Duchenne Muscular Dystrophy –⁠ tracheostomy –⁠ tracheomalacia –⁠ tracheostenosis –⁠ tracheo-arterial fistula

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Assoc. Prof. MUDr. Josef Hoder, CSc., in the memories of his colleagues and friends

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Article was published in

Anaesthesiology and Intensive Care Medicine

2009 Issue 2