A fatal complication of tracheostomy in a 13-year-old patient with Duchenne Muscular Dystrophy – case report
Authors:
Stříteská Jana 1; Pařízková Renata 1; Dostál Pavel 1; Hoffmann Petr 2; Černý Vladimír 1
Authors‘ workplace:
Klinika anesteziologie, resuscitace a intenzivní medicíny, UK v Praze, LF v Hradci Králové, Fakultní nemocnice Hradec Králové
1; Radiologická klinika, Fakultní nemocnice Hradec Králové
2
Published in:
Anest. intenziv. Med., 20, 2009, č. 2, s. 107-112
Category:
Intesive Care Medicine - Case Report
Overview
The authors describe a case of a 13-year-old boy suffering from Duchenne muscular dystrophy. Permanent mechanical ventilation was necessary due to the patient’s progressive chronic respiratory insufficiency. A surgical tracheostomy was complicated by the development of tracheal stenosis managed with special types of tracheostomy tubes. A tracheo-arterial fistula developed as a result of progression of skeletal chest deformities and the tracheal stenosis. The patient died of massive arterial haemorrhage from the fistula formed between the trachea and the brachiocephalic trunk.
Keywords:
Duchenne Muscular Dystrophy – tracheostomy – tracheomalacia – tracheostenosis – tracheo-arterial fistula
Sources
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Anaesthesiology, Resuscitation and Inten Intensive Care MedicineArticle was published in
Anaesthesiology and Intensive Care Medicine
2009 Issue 2
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