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Gastrointestinálny stromálny tumor (GIST) s glandulárnou zložkou. Popis neobvyklého prípadu
: M. Zámečník 1; B. Sosna 2; A. Chlumská 1
: Šikl’s Department of Pathology, Faculty Hospital Charles University, Pilsen, Czech Republic 1; Laboratory of Surgical Pathology, Pilsen, Czech Republic 2
: Čes.-slov. Patol., 41, 2005, No. 4, p. 150-156
: Original Article
Popísaný je neobvyklý prípad gastrointestinálneho stromálneho tumoru (GIST) s glandulárnou zložkou. Šlo o tumor gastrického fundu u 93-ročnej ženy. Histológia lézie bola tvorená diferencovanou vretenobunkovou štruktúrou typického GIST-u, v ktorej boli difúzne prítomné z časti cystické žliazky. Kolumnárny epitel žliazok bol podobný pylorickému a foveolárnemu typu, s ložiskami intestinálnej metaplázie a miestami s dyspláziami. Stromálna zložka tumoru bola imunohistochemicky pozitívna na CD117 (c-kit) a CD34, negatívne boli myoidné a neuroidné markery. Elektronmikroskopicky šlo o nediferencované vretenovité bunky. Sliznica a submukóza v blízkosti tumoru vykazovali fokálne známky gastritis cystica profunda so žliazkami podobnými ako vnútri tumoru. V histogenéze tumoru je predpokladaná kolízia GIST-u a gastritis cystica profunda.
Kľúčové slová:
gastrointestinálny stromálny tumor – adenokarcinóm – gastritis cystica profunda – adenosarkóm – karcinosarkóm – žalúdok
Labels
Anatomical pathology Forensic medical examiner Toxicology
Article was published inCzecho-Slovak Pathology
2005 Issue 4-
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