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Progressive supranuclear palsy


Authors: T. Bartošová 1;  J. Klempíř- 1 3
Authors‘ workplace: Neurologická klinika a Centrum klinických neurověd, 1. LF UK a VFN v Praze 1;  Anatomický ústav, 1. LF UK v Praze 2;  Evropská referenční síť pro vzácná neurologická onemocnění 3
Published in: Cesk Slov Neurol N 2020; 83/116(6): 584-601
Category: Review Article
doi: https://doi.org/10.48095/cccsnn2020584

Overview

Progressive supranuclear palsy is a tauopathy belonging to atypical Parkinsonian syndromes. The main clinical symptoms include oculomotor dysfunctions, early postural instability, symmetrical hypokinetic-rigid syndrome with axial predominance and cognitive decline. The symptom variability and rate of progression depend on disease subtype. Dia­gnostics are based on clinical symptoms; MRI remains the most useful auxiliary method. The article is focused mainly on clinical perspectives and recent dia­g­nostic approaches considering the latest recommendations. Symptomatic therapy remains of great importance as causal treatment is still lacking.

Keywords:

progressive supranuclear palsy – vertical gaze palsy – tauopathy – postural instability – parkinsonism – cognitive decline – Levodopa – amantadine


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Paediatric neurology Neurosurgery Neurology

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Czech and Slovak Neurology and Neurosurgery

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