Urethral duplication in children – three cases
Authors:
Josef Sedláček; Marcel Drlík; Radim Kočvara
Authors‘ workplace:
Urologická klinika VFN a 1. LF UK Praha
Published in:
Ces Urol 2022; 26(2): 139-145
Category:
Case reports
Overview
Urethral duplication represents a spectrum of rare congenital anomalies with different phenotypes, the common feature of which is the duplication of a part or complete urethra. This defect should be kept in mind whenever, in addition to the normally located urethral orifice on the glans, an additional orifice is found on the dorsal or ventral surface of the penis, scrotum or perineum. The supernumerary orifice, which may be hidden under the nonretractile foreskin in children with phimosis, should also be looked for in patients with significant dorsal penile angulation. The purpose of the work up is to assess the extent of the supernumerary urethra and its possible communication with the normal urethra or bladder. Treatment is individualized. Focused on symptoms and risks. In this paper, we describe 3 cases of urethral duplication in children and summarize the current view on the diagnosis and treatment of this anomaly.
Keywords:
Urethral duplication – Effmann´s classification – dorsal angulation of penis
Sources
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Labels
Paediatric urologist Nephrology UrologyArticle was published in
Czech Urology
2022 Issue 2
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