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The Coincidence of the Junction Layer of Inner and Outer Photoreceptors Segments (IS/OS) Defects Localization on SD OCT and Functional Defects in Case of Stargardt Disease – a Case Report


Authors: E. Rencová;  J. Studnička;  J. Marak;  H. Dvořáková;  H. Langrová
Authors‘ workplace: Oční klinika FN a LF UK Hradec Králové, Přednosta prof. MUDr. Pavel Rozsíval, CSc., FEBO
Published in: Čes. a slov. Oftal., 68, 2012, No. 2, p. 84-88
Category: Case Report

Overview

Case report of the different visual functions of the right and left eye of 60-years old man with Stargardt disease is presented. The difference in best corrected visual acuity between both eyes is accompanied with corresponding various alteration of the central retinal activity using multifocal electroretinography (mfERG) and asymmetrical defects of the IS/OS photoreceptor junction using HD-OCT.

Key words:
HD OCT, IS/OS photoreceptors junction, Stargardt disease, central retinal dystrophy, multifocal electroretinography (mfERG)


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Ophthalmology
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