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Consensual guidelines of the Czech National Haemophilia Programme (CNHP) for the diagnosis and treatment of patients with congenital haemophilia and inhibitors to FVIII/FIX


Authors: P. Smejkal 1;  J. Blatný 2;  A. Hluší 3;  R. Hrdličková 4;  V. Komrska 5;  M. Penka 1;  J. Šlechtová 6;  J. Blatný 2;  B. Blažek 7;  Z. Čermáková 4;  Z. Černá 8;  P. Ďulíček 9;  J. Hak 10;  A. Hluší 3;  R. Hrdličková 4;  V. Komrska 5;  P. Ovesná 11;  D. Pospíšilová 12;  D. Procházková 13;  P. Smejkal 1;  J. Šlechtová 6;  P. Timr 14;  J. Ullrychová 15;  I. Vonke 16;  L. Walterová 17;  M. Penka 1
Authors‘ workplace: Oddělení klinické hematologie, Fakultní nemocnice Brno 1;  Oddělení dětské hematologie, Fakultní nemocnice Brno 2;  Hemato-onkologická klinika, Fakultní nemocnice Olomouc 3;  Klinika hematoonkologie a Krevní centrum, Fakultní nemocnice Ostrava 4;  Klinika dětské hematologie a onkologie, Fakultní nemocnice v Motole, Praha 5;  Ústav klinické biochemie a hematologie, Fakultní nemocnice Plzeň 6;  Klinika dětského lékařství, Fakultní nemocnice Ostrava 7;  Dětská klinika, Fakultní nemocnice Plzeň 8;  IV. Interní hematologická klinika, Fakultní nemocnice Hradec Králové 9;  Dětská klinika, Fakultní nemocnice Hradec Králové 10;  Institut biostatistiky a analýz Lékařské fakulty, Masarykova univerzita, Brno 11;  Dětská klinika, Fakultní nemocnice Olomouc 12;  Dětská klinika, Krajská zdravotní a. s., Masarykova nemocnice v Ústí nad Labem 13;  Dětské oddělení, Nemocnice České Budějovice 14;  Oddělení klinické hematologie, Krajská zdravotní a. s., Masarykova nemocnice v Ústí nad Labem 15;  Oddělení klinické hematologie, Nemocnice České Budějovice 16;  Oddělení klinické hematologie, Krajská nemocnice Liberec 17
Published in: Transfuze Hematol. dnes,22, 2016, No. 1, p. 44-54.
Category: Comprehensive Reports, Original Papers, Case Reports

Pozn:
*Pracovní skupina ČNHP pro standardy
**Jménem Koordinační rady a Výkonné rady ČNHP

Overview

The aim of these guidelines is to set-up and standardized diagnostic as well as therapeutic approaches to patients suffering from congenital haemophilia and factor VIII or factor IX inhibitors.

Key words:
haemophilia – guidelines – treatment – inhibitor – surgery


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Haematology Internal medicine Clinical oncology

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